PRAGUE MEDICAL REPORT, Vol 125 No 1 (2024), 69–78
Gorlin-Goltz Syndrome – A Rare Case Entity in Young Child
Shovita Mondal, Nikil Kumar Jain, Abhishek Dutta, Nishant, Abhijit Dutta, Moushumi Shil, Suman Sen
DOI: https://doi.org/10.14712/23362936.2024.7
zveřejněno: 21. 02. 2024
Abstract
Gorlin-Goltz syndrome (GGS) is an infrequent multisystemic disease with an autosomal dominant trait, which depicted presence of numerous basal cell carcinoma in conjunction with multiorgan abnormalities. This syndrome may be diagnosed early by a dentist by routine radiographic exams in the first decade of life, since the keratocystic odontogenic tumour are usually one of the first manifestations of the syndrome. This article includes a case report of the GGS with regard to its history, incidence, etiology, features, investigations, diagnostic criteria, keratocystic odontogenic tumour and treatment modalities.
klíčová slova: Nevoid basal cell carcinoma; Odontogenic keratocyst; Carnoy’s solution; “En-bloc” resection; Marsupialization; Bifid rib
Gorlin-Goltz Syndrome – A Rare Case Entity in Young Child is licensed under a Creative Commons Attribution 4.0 International License.
167 x 240 mm
vychází: 4 x ročně
cena tištěného čísla: 450 Kč
ISSN: 1214-6994
E-ISSN: 2336-2936