PRAGUE MEDICAL REPORT, Vol 116 No 3 (2015), 181–192
Ormond’s Disease – IgG4-related Disease
Miroslav Průcha, Ivan Kolombo, Petr Štádler
DOI: https://doi.org/10.14712/23362936.2015.57
published online: 09. 10. 2015
abstract
Ormond’s disease is a relatively rare disease with unclear etiology, characterized by chronic periaortitis and retroperitoneal fibrosis. The inflammatory process affects the infrarenal part of the abdominal aorta and the iliac arteries, and the presence of infiltrates encasing the ureters and inferior vena cava. This disease is currently classed as an IgG4-related disease. In our review we analyse the clinical history, diagnostic approaches, surgical and immunosuppressive therapies.
keywords: Ormond’s disease; Periaortitis; Hydronefrosis; Surgical treatment; Immunosuppression
167 x 240 mm
periodicity: 4 x per year
print price: 450 czk
ISSN: 1214-6994
E-ISSN: 2336-2936